| Preferred Name |
immunoglobulin light chain amyloidosis |
| Synonyms |
Primary systemic AL amyloidosis Light chain amyloidosis AL amyloidosis Systemic AL amyloidsis Primary systemic amyloidosis Amyloidosis primary systemic Primary AL amyloidosis |
| Definitions |
An amyloidosis that is characterized by misfolded and aggregated amyloidogenic immunoglobulin light chains produced by marrow clonal plasma cells. |
| ID |
http://purl.obolibrary.org/obo/DOID_0080933 |
| database_cross_reference |
ICD10CM:E85.81 MESH:D000075363 |
| definition |
An amyloidosis that is characterized by misfolded and aggregated amyloidogenic immunoglobulin light chains produced by marrow clonal plasma cells. |
| disease has basis in | |
| disease has location |
http://purl.obolibrary.org/obo/UBERON_0002107 http://purl.obolibrary.org/obo/UBERON_0001021 |
| has exact synonym |
Primary systemic AL amyloidosis Light chain amyloidosis AL amyloidosis Systemic AL amyloidsis Primary systemic amyloidosis Amyloidosis primary systemic Primary AL amyloidosis |
| has_obo_namespace |
disease_ontology |
| id |
DOID:0080933 |
| label |
immunoglobulin light chain amyloidosis |
| notation |
DOID:0080933 |
| prefLabel |
immunoglobulin light chain amyloidosis |
| subClassOf |
http://purl.obolibrary.org/obo/DOID_557 http://purl.obolibrary.org/obo/DOID_114 http://purl.obolibrary.org/obo/DOID_409 |
| Delete | Mapping To | Ontology | Source |
|---|---|---|---|
| http://purl.bioontology.org/ontology/MESH/D000075363 | Medical Subject Headings | LOOM |