Preferred Name

主动脉弓离断 / Interrupted aortic arch

Definitions

A congenital cardiovascular malformation in which there is an absence of luminal continuity between the ascending and descending aorta. This includes luminal atresia with discontinuity between the aortic segments and also luminal atresia with fibrous continuity between the aortic segments. Interrupted aortic arch is defined as the loss of luminal continuity between the ascending and descending aorta. In most cases, blood flow to the descending thoracic aorta is through a patent arterial duct, and there is a large ventricular septal defect. Arch interruption is further defined by site of interruption. In type A, interruption is distal to the left subclavian artery; in type B, interruption is between the left carotid and left subclavian arteries; and in type C, interruption occurs between the innominate and left carotid arteries.

ID

http://purl.bmicc.cn/ontology/ICD11CN/LA8B.22

definition

A congenital cardiovascular malformation in which there is an absence of luminal continuity between the ascending and descending aorta. This includes luminal atresia with discontinuity between the aortic segments and also luminal atresia with fibrous continuity between the aortic segments. Interrupted aortic arch is defined as the loss of luminal continuity between the ascending and descending aorta. In most cases, blood flow to the descending thoracic aorta is through a patent arterial duct, and there is a large ventricular septal defect. Arch interruption is further defined by site of interruption. In type A, interruption is distal to the left subclavian artery; in type B, interruption is between the left carotid and left subclavian arteries; and in type C, interruption occurs between the innominate and left carotid arteries.

hasDbXref

http://id.who.int/icd/release/11/2019-04/mms/1769930414

label

主动脉弓离断 / Interrupted aortic arch

mappingRelation

http://purl.bmicc.cn/ontology/ICD10CN/Q25

notation

LA8B.22

prefixIRI

ICD11CN:LA8B.22

prefLabel

主动脉弓离断 / Interrupted aortic arch

subClassOf

http://purl.bmicc.cn/ontology/ICD11CN/LA8B.2

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http://purl.bioontology.org/ontology/OMIM/MTHU015284 Online Mendelian Inheritance in Man LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C98958 National Cancer Institute Thesaurus LOOM