Medical Subject Headings

Last uploaded: November 5, 2019
Preferred Name

Fibrillins

Synonyms

Fibrillin

Definitions

A family of extracellular matrix glycoproteins that is structurally similar to LATENT TGF-BETA BINDING PROTEINS, but contain additional TGF-beta binding domains, in addition to unique domains at their N and C-terminals. Fibrillins assemble into 10-12 nm MICROFIBRILS that function in a variety of cell interactions with the EXTRACELLULAR MATRIX and developmental processes such as ELASTIC TISSUE maintenance and assembly, and the targeting of growth factors to the extracellular matrix.

ID

http://purl.bioontology.org/ontology/MESH/D000071837

altLabel

Fibrillin

AQL

AD AE AG AI AN BI BL CF CH CL CS DE DF EC GE HI IM IP ME PD PH PK PO RE SD ST TO TU UL UR

cui

C4255101

DC

1

definition

A family of extracellular matrix glycoproteins that is structurally similar to LATENT TGF-BETA BINDING PROTEINS, but contain additional TGF-beta binding domains, in addition to unique domains at their N and C-terminals. Fibrillins assemble into 10-12 nm MICROFIBRILS that function in a variety of cell interactions with the EXTRACELLULAR MATRIX and developmental processes such as ELASTIC TISSUE maintenance and assembly, and the targeting of growth factors to the extracellular matrix.

DX

20170101

HN

2017; use FIBRILLIN 1985-2016

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000032

http://purl.bioontology.org/ontology/MESH/Q000138

http://purl.bioontology.org/ontology/MESH/Q000737

http://purl.bioontology.org/ontology/MESH/Q000493

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000506

http://purl.bioontology.org/ontology/MESH/Q000819

http://purl.bioontology.org/ontology/MESH/Q000187

http://purl.bioontology.org/ontology/MESH/Q000096

http://purl.bioontology.org/ontology/MESH/Q000037

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000592

http://purl.bioontology.org/ontology/MESH/Q000528

http://purl.bioontology.org/ontology/MESH/Q000008

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000648

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000633

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000009

http://purl.bioontology.org/ontology/MESH/Q000302

http://purl.bioontology.org/ontology/MESH/Q000502

http://purl.bioontology.org/ontology/MESH/Q000494

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000600

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000172

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000627

Inverse of RB

0

Inverse of SIB

http://purl.bioontology.org/ontology/MESH/D055511

http://purl.bioontology.org/ontology/MESH/D020410

http://purl.bioontology.org/ontology/MESH/D007797

http://purl.bioontology.org/ontology/MESH/D053480

http://purl.bioontology.org/ontology/MESH/D008562

http://purl.bioontology.org/ontology/MESH/D018993

http://purl.bioontology.org/ontology/MESH/D000071816

http://purl.bioontology.org/ontology/MESH/D053330

http://purl.bioontology.org/ontology/MESH/D009088

http://purl.bioontology.org/ontology/MESH/D019096

http://purl.bioontology.org/ontology/MESH/D053675

http://purl.bioontology.org/ontology/MESH/D000514

http://purl.bioontology.org/ontology/MESH/D014156

http://purl.bioontology.org/ontology/MESH/D006466

http://purl.bioontology.org/ontology/MESH/D064235

http://purl.bioontology.org/ontology/MESH/D053482

http://purl.bioontology.org/ontology/MESH/D013975

http://purl.bioontology.org/ontology/MESH/D004549

http://purl.bioontology.org/ontology/MESH/D060749

http://purl.bioontology.org/ontology/MESH/D017293

http://purl.bioontology.org/ontology/MESH/D019063

http://purl.bioontology.org/ontology/MESH/D000075385

http://purl.bioontology.org/ontology/MESH/D050958

http://purl.bioontology.org/ontology/MESH/D000071232

http://purl.bioontology.org/ontology/MESH/D028341

http://purl.bioontology.org/ontology/MESH/D058574

http://purl.bioontology.org/ontology/MESH/D053264

http://purl.bioontology.org/ontology/MESH/D005353

http://purl.bioontology.org/ontology/MESH/D000979

http://purl.bioontology.org/ontology/MESH/D013954

http://purl.bioontology.org/ontology/MESH/D007781

http://purl.bioontology.org/ontology/MESH/D003094

http://purl.bioontology.org/ontology/MESH/D014409

http://purl.bioontology.org/ontology/MESH/D011486

http://purl.bioontology.org/ontology/MESH/D053779

http://purl.bioontology.org/ontology/MESH/D000071096

http://purl.bioontology.org/ontology/MESH/D050718

http://purl.bioontology.org/ontology/MESH/D000683

http://purl.bioontology.org/ontology/MESH/D001360

http://purl.bioontology.org/ontology/MESH/D001212

http://purl.bioontology.org/ontology/MESH/D007265

http://purl.bioontology.org/ontology/MESH/D011509

http://purl.bioontology.org/ontology/MESH/D000515

http://purl.bioontology.org/ontology/MESH/D064236

http://purl.bioontology.org/ontology/MESH/D051722

http://purl.bioontology.org/ontology/MESH/D006442

http://purl.bioontology.org/ontology/MESH/D015676

http://purl.bioontology.org/ontology/MESH/D003115

http://purl.bioontology.org/ontology/MESH/D053674

http://purl.bioontology.org/ontology/MESH/D053282

http://purl.bioontology.org/ontology/MESH/D051152

http://purl.bioontology.org/ontology/MESH/D053495

http://purl.bioontology.org/ontology/MESH/D012795

http://purl.bioontology.org/ontology/MESH/D054304

Machine permutation

2017; see FIBRILLIN 1985-2016

Mapped from

http://purl.bioontology.org/ontology/MESH/C493782

MDA

20160708

MMR

20160415

MN

D09.400.430.875

D12.776.395.341

D12.776.860.300.400

notation

D000071837

prefLabel

Fibrillins

TERMUI

T000896836

T000896835

TH

NLM (2017)

NLM (1985)

tui

T116

T123

subClassOf

http://purl.bioontology.org/ontology/MESH/D006023

http://purl.bioontology.org/ontology/MESH/D016326

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