Medical Subject Headings

Last uploaded: November 5, 2019
Preferred Name

Argininosuccinate Lyase

Synonyms

Argininosuccinase

Definitions

An enzyme of the urea cycle which splits argininosuccinate to fumarate plus arginine. Its absence leads to the metabolic disease ARGININOSUCCINIC ACIDURIA in man. EC 4.3.2.1.

ID

http://purl.bioontology.org/ontology/MESH/D001123

altLabel

Argininosuccinase

Lyase, Argininosuccinate

N-(L-Argininosuccinate) arginine-lyase

AQL

AD AE AI AN BI BL CF CH CL CS DE EC GE HI IM IP ME PD PH PK PO RE SD ST TO TU UL UR

cui

C0003775

DC

1

definition

An enzyme of the urea cycle which splits argininosuccinate to fumarate plus arginine. Its absence leads to the metabolic disease ARGININOSUCCINIC ACIDURIA in man. EC 4.3.2.1.

DX

19910101

EC

deficiency:Argininosuccinic Aciduria

FX

D056807

HN

1991(1975); use LYASES 1975-1990

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000032

http://purl.bioontology.org/ontology/MESH/Q000138

http://purl.bioontology.org/ontology/MESH/Q000737

http://purl.bioontology.org/ontology/MESH/Q000493

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000506

http://purl.bioontology.org/ontology/MESH/Q000187

http://purl.bioontology.org/ontology/MESH/Q000096

http://purl.bioontology.org/ontology/MESH/Q000037

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000592

http://purl.bioontology.org/ontology/MESH/Q000528

http://purl.bioontology.org/ontology/MESH/Q000008

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000648

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000633

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000009

http://purl.bioontology.org/ontology/MESH/Q000302

http://purl.bioontology.org/ontology/MESH/Q000502

http://purl.bioontology.org/ontology/MESH/Q000494

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000600

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000627

Inverse of RB

EC 4.3.2.1

Inverse of RO

http://purl.bioontology.org/ontology/MESH/D056807

Inverse of SIB

http://purl.bioontology.org/ontology/MESH/D000264

Machine permutation

1991; see LYASES 1975-1990

Mapped from

http://purl.bioontology.org/ontology/MESH/C449683

http://purl.bioontology.org/ontology/MESH/C019726

http://purl.bioontology.org/ontology/MESH/C087900

MDA

19741119

MMR

20090706

MN

D08.811.520.232.300.400

notation

D001123

prefLabel

Argininosuccinate Lyase

RR

9027-34-3 (CAS RN)

TERMUI

T003395

T003396

TH

NLM (1975)

UNK (19XX)

tui

T116

T126

subClassOf

http://purl.bioontology.org/ontology/MESH/D019760

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http://purl.bioontology.org/ontology/LNC/LP15418-4 Logical Observation Identifier Names and Codes CUI
http://purl.bioontology.org/ontology/LNC/LP15418-4 Logical Observation Identifier Names and Codes LOOM
http://purl.obolibrary.org/obo/PR_000004373 Protein Ontology LOOM
http://purl.bioontology.org/ontology/OMIM/608310 Online Mendelian Inheritance in Man LOOM
http://purl.bioontology.org/ontology/LNC/MTHU008485 Logical Observation Identifier Names and Codes CUI
http://purl.bioontology.org/ontology/LNC/MTHU008485 Logical Observation Identifier Names and Codes LOOM