Definitions |
Hereditary disorder consisting of multiple basal cell carcinomas, odontogenic keratocysts, and multiple skeletal defects, e.g., frontal and temporoparietal bossing, bifurcated and splayed ribs, kyphoscoliosis, fusion of vertebrae, and cervicothoracic spina bifida. Genetic transmission is autosomal dominant.
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Fifth Phacomatoses Multiple Basal Cell Nevi, Odontogenic Keratocysts, and Skeletal Anomalies Gorlin Syndrome Syndrome, Gorlin-Goltz Gorlin-Goltz Syndrome NBCCS Fifth Phacomatosis Gorlin Goltz Syndrome Syndrome, Gorlin Nevus Syndrome, Basal Cell Nevoid Basal Cell Carcinoma Syndrome
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definition |
Hereditary disorder consisting of multiple basal cell carcinomas, odontogenic keratocysts, and multiple skeletal defects, e.g., frontal and temporoparietal bossing, bifurcated and splayed ribs, kyphoscoliosis, fusion of vertebrae, and cervicothoracic spina bifida. Genetic transmission is autosomal dominant.
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