Preferred Name |
Cystathionine gamma-Lyase |
Synonyms |
gamma-Lyase, Cystathionine |
Definitions |
A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyzes the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate. EC 4.4.1.1. |
ID |
http://purl.bioontology.org/ontology/MESH/D003542 |
altLabel |
gamma-Lyase, Cystathionine Cystine Desulfhydrase gamma Cystathionase Desulfohydrolase, Cystine Homoserine Deaminase L-Cystathionine cysteine-lyase (deaminating) gamma-Cystathionase Deaminase, Homoserine Homoserine Dehydratase Cystine Desulfohydrolase Cystathionine gamma Lyase Desulfhydrase, Cystine Cysteine Desulfhydrase Cystathionase Dehydratase, Homoserine Desulfhydrase, Cysteine |
AN |
/defic: consider also CYSTATHIONINE /urine (IM) + AMINO ACID METABOLISM, INBORN ERRORS (IM) |
AQL |
AD AE AI AN BI BL CF CH CL CS DE DF EC GE HI IM IP ME PD PH PK PO RE SD ST TO TU UL UR |
cui |
C0010642 |
DC |
1 |
definition |
A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyzes the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate. EC 4.4.1.1. |
DX |
19910101 |
HN |
91(75); was see under LYASES 1975-90 |
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000032 http://purl.bioontology.org/ontology/MESH/Q000138 http://purl.bioontology.org/ontology/MESH/Q000737 http://purl.bioontology.org/ontology/MESH/Q000493 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000506 http://purl.bioontology.org/ontology/MESH/Q000187 http://purl.bioontology.org/ontology/MESH/Q000096 http://purl.bioontology.org/ontology/MESH/Q000037 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000592 http://purl.bioontology.org/ontology/MESH/Q000528 http://purl.bioontology.org/ontology/MESH/Q000008 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000648 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000633 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000009 http://purl.bioontology.org/ontology/MESH/Q000302 http://purl.bioontology.org/ontology/MESH/Q000502 http://purl.bioontology.org/ontology/MESH/Q000494 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000600 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000172 |
Inverse of RB |
EC 4.4.1.1 |
Inverse of SIB | |
Machine permutation |
91; was see under LYASES 1975-90 |
Mapped from |
http://purl.bioontology.org/ontology/MESH/C400145 http://purl.bioontology.org/ontology/MESH/C079405 http://purl.bioontology.org/ontology/MESH/C562680 http://purl.bioontology.org/ontology/MESH/C000621859 |
MDA |
19741111 |
MMR |
20030709 |
MN |
D08.811.520.300.250 |
notation |
D003542 |
prefLabel |
Cystathionine gamma-Lyase |
RR |
9012-96-8 (CAS RN) |
TERMUI |
T010276 T010274 T010273 T010271 T010275 T010277 T010272 T010278 |
TH |
NLM (1975) UNK (19XX) NLM (1989) |
tui |
T116 T126 |
subClassOf |
Delete | Mapping To | Ontology | Source |
---|---|---|---|
http://purl.bioontology.org/ontology/OMIM/607657 | Online Mendelian Inheritance in Man | LOOM | |
http://purl.obolibrary.org/obo/PR_000006004 | Protein Ontology | LOOM |