Medical Subject Headings

Last uploaded: November 5, 2019
Preferred Name

Cystathionine gamma-Lyase

Synonyms

gamma-Lyase, Cystathionine

Definitions

A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyzes the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate. EC 4.4.1.1.

ID

http://purl.bioontology.org/ontology/MESH/D003542

altLabel

gamma-Lyase, Cystathionine

Cystine Desulfhydrase

gamma Cystathionase

Desulfohydrolase, Cystine

Homoserine Deaminase

L-Cystathionine cysteine-lyase (deaminating)

gamma-Cystathionase

Deaminase, Homoserine

Homoserine Dehydratase

Cystine Desulfohydrolase

Cystathionine gamma Lyase

Desulfhydrase, Cystine

Cysteine Desulfhydrase

Cystathionase

Dehydratase, Homoserine

Desulfhydrase, Cysteine

AN

/defic: consider also CYSTATHIONINE /urine (IM) + AMINO ACID METABOLISM, INBORN ERRORS (IM)

AQL

AD AE AI AN BI BL CF CH CL CS DE DF EC GE HI IM IP ME PD PH PK PO RE SD ST TO TU UL UR

cui

C0010642

DC

1

definition

A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyzes the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate. EC 4.4.1.1.

DX

19910101

HN

91(75); was see under LYASES 1975-90

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000032

http://purl.bioontology.org/ontology/MESH/Q000138

http://purl.bioontology.org/ontology/MESH/Q000737

http://purl.bioontology.org/ontology/MESH/Q000493

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000506

http://purl.bioontology.org/ontology/MESH/Q000187

http://purl.bioontology.org/ontology/MESH/Q000096

http://purl.bioontology.org/ontology/MESH/Q000037

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000592

http://purl.bioontology.org/ontology/MESH/Q000528

http://purl.bioontology.org/ontology/MESH/Q000008

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000648

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000633

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000009

http://purl.bioontology.org/ontology/MESH/Q000302

http://purl.bioontology.org/ontology/MESH/Q000502

http://purl.bioontology.org/ontology/MESH/Q000494

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000600

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000172

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000627

Inverse of RB

EC 4.4.1.1

Inverse of SIB

http://purl.bioontology.org/ontology/MESH/D007791

Machine permutation

91; was see under LYASES 1975-90

Mapped from

http://purl.bioontology.org/ontology/MESH/C400145

http://purl.bioontology.org/ontology/MESH/C079405

http://purl.bioontology.org/ontology/MESH/C562680

http://purl.bioontology.org/ontology/MESH/C000621859

http://purl.bioontology.org/ontology/MESH/C073674

http://purl.bioontology.org/ontology/MESH/C000604139

MDA

19741111

MMR

20030709

MN

D08.811.520.300.250

notation

D003542

prefLabel

Cystathionine gamma-Lyase

RR

9012-96-8 (CAS RN)

TERMUI

T010276

T010274

T010273

T010271

T010275

T010277

T010272

T010278

TH

NLM (1975)

UNK (19XX)

NLM (1989)

tui

T116

T126

subClassOf

http://purl.bioontology.org/ontology/MESH/D013437

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http://purl.bioontology.org/ontology/OMIM/607657 Online Mendelian Inheritance in Man LOOM
http://purl.obolibrary.org/obo/PR_000006004 Protein Ontology LOOM