loading...| Preferred Name |
Subacute Sclerosing Panencephalitis |
| Synonyms |
Leukoencephalitides, Subacute Sclerosing |
| Definitions |
A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8) |
| ID |
http://purl.bioontology.org/ontology/MESH/D013344 |
| altLabel |
Leukoencephalitides, Subacute Sclerosing Subacute Sclerosing Panencephalitides SSPE Sclerosing Panencephalitis, Subacute Encephaltis, Inclusion Body, Measles Subacute Sclerosing Leukoencephalitides Measles Inclusion Body Encephalitis Panencephalitides, Subacute Sclerosing Subacute Sclerosing Leukoencephalitis Inclusion Body Encephalitis, Measles Van Bogaert Leukoencephalitis Leukoencephalitis, Van Bogaerts Van Bogaert's Leukoencephalitis Leukoencephalitis, Subacute Sclerosing Sclerosing Panencephalitides, Subacute Panencephalitis, Subacute Sclerosing Leukoencephalitis, Van Bogaert Sclerosing Leukoencephalitides, Subacute Van Bogaerts Leukoencephalitis Leukoencephalitis, Van Bogaert's Sclerosing Leukoencephalitis, Subacute |
| AQL |
BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH TM UR VE VI |
| cui |
C0038522 |
| DC |
1 |
| definition |
A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8) |
| DX |
19710101 |
| HN |
71; VAN BOGAERT'S LEUKOENCEPHALITIS was see under SUBACUTE SCLEROSING PANENCEPHALITIS 1971-78; was see under CEREBRAL SCLEROSIS, DIFFUSE 1963-70 |
| Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000401 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000523 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000635 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000209 |
| Inverse of RO | |
| Inverse of SIB |
http://purl.bioontology.org/ontology/MESH/D000163 http://purl.bioontology.org/ontology/MESH/D004671 http://purl.bioontology.org/ontology/MESH/D020803 http://purl.bioontology.org/ontology/MESH/D000386 http://purl.bioontology.org/ontology/MESH/D011021 http://purl.bioontology.org/ontology/MESH/D000453 http://purl.bioontology.org/ontology/MESH/D016097 http://purl.bioontology.org/ontology/MESH/D004683 http://purl.bioontology.org/ontology/MESH/D016182 http://purl.bioontology.org/ontology/MESH/D004859 http://purl.bioontology.org/ontology/MESH/D007968 |
| Machine permutation |
71; VAN BOGAERT'S LEUKOENCEPHALITIS was see under SUBACUTE SCLEROSING PANENCEPHALITIS 1971-78; was see under CEREBRAL SCLEROSIS, DIFFUSE 1963-70 |
| Mapped from | |
| MDA |
19990101 |
| MMR |
20150702 |
| MN |
C10.228.140.430.520.750.600 C02.290.700 C02.839.862 C02.782.580.600.500.500.800 C02.182.525.600 C10.228.228.245.340.600 C10.228.228.399.750.600 |
| notation |
D013344 |
| OL |
use SUBACUTE SCLEROSING PANENCEPHALITIS to search VAN BOGAERT'S LEUKOENCEPHALITIS 1971-78; use CEREBRAL SCLEROSIS, DIFFUSE 1966-70 |
| prefLabel |
Subacute Sclerosing Panencephalitis |
| TERMUI |
T370626 T039187 T039181 T039186 T039185 T039184 T370627 T370628 T039183 T039182 T039180 |
| TH |
NLM (1993) UNK (19XX) NLM (1990) NLM (1971) NLM (2000) ORD (2010) NLM (1995) OMIM (2013) |
| tui |
T047 |
| subClassOf |
http://purl.bioontology.org/ontology/MESH/D018792 |