Prion Diseases

Transmissible Spongiform Encephalopathy

A group of genetic, infectious, or sporadic degenerative human and animal nervous system disorders associated with abnormal PRIONS. These diseases are characterized by conversion of the normal prion protein to an abnormal configuration via a post-translational process. In humans, these conditions generally feature DEMENTIA; ATAXIA; and a fatal outcome. Pathologic features include a spongiform encephalopathy without evidence of inflammation. The older literature occasionally refers to these as unconventional SLOW VIRUS DISEASES. (From Proc Natl Acad Sci USA 1998 Nov 10;95(23):13363-83)

http://purl.bioontology.org/ontology/MESH/D017096

Transmissible Spongiform Encephalopathy

Prion Disease

Encephalopathies, Spongiform, Transmissible

Prion-Associated Disorders

Spongiform Encephalopathies, Transmissible

Dementias, Transmissible

Disorder, Prion-Induced

Dementia, Transmissible

Prion Induced Disorder

Human Transmissible Spongiform Encephalopathies, Inherited

Prion Protein Diseases

Prion Protein Disease

Transmissible Dementias

Transmissible Spongiform Encephalopathies

Prion-Induced Disorders

Inherited Human Transmissible Spongiform Encephalopathies

Prion-Induced Disorder

Disorders, Prion-Induced

Transmissible Dementia

Spongiform Encephalopathy, Transmissible

Encephalopathy, Transmissible Spongiform

Encephalopathies, Transmissible Spongiform

GEN or unspecified: prefer specifics

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH TM UR VE VI

C0162534

C0751645

1

A group of genetic, infectious, or sporadic degenerative human and animal nervous system disorders associated with abnormal PRIONS. These diseases are characterized by conversion of the normal prion protein to an abnormal configuration via a post-translational process. In humans, these conditions generally feature DEMENTIA; ATAXIA; and a fatal outcome. Pathologic features include a spongiform encephalopathy without evidence of inflammation. The older literature occasionally refers to these as unconventional SLOW VIRUS DISEASES. (From Proc Natl Acad Sci USA 1998 Nov 10;95(23):13363-83)

19930101

1993

http://purl.bioontology.org/ontology/MESH/Q000401

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000635

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/D012608

http://purl.bioontology.org/ontology/MESH/D012897

http://purl.bioontology.org/ontology/MESH/D000070627

http://purl.bioontology.org/ontology/MESH/D052879

http://purl.bioontology.org/ontology/MESH/D020361

http://purl.bioontology.org/ontology/MESH/D020314

http://purl.bioontology.org/ontology/MESH/D020271

http://purl.bioontology.org/ontology/MESH/D020806

http://purl.bioontology.org/ontology/MESH/D001922

http://purl.bioontology.org/ontology/MESH/D024801

http://purl.bioontology.org/ontology/MESH/D009187

http://purl.bioontology.org/ontology/MESH/D000069544

http://purl.bioontology.org/ontology/MESH/D004679

http://purl.bioontology.org/ontology/MESH/D019578

http://purl.bioontology.org/ontology/MESH/D008590

http://purl.bioontology.org/ontology/MESH/D020805

http://purl.bioontology.org/ontology/MESH/D020802

http://purl.bioontology.org/ontology/MESH/D020819

http://purl.bioontology.org/ontology/MESH/D010300

http://purl.bioontology.org/ontology/MESH/D016262

http://purl.bioontology.org/ontology/MESH/D020807

http://purl.bioontology.org/ontology/MESH/D020961

http://purl.bioontology.org/ontology/MESH/D016472

http://purl.bioontology.org/ontology/MESH/D057177

1993

http://purl.bioontology.org/ontology/MESH/C564678

http://purl.bioontology.org/ontology/MESH/C535800

19920522

20150623

C10.228.228.800

C10.574.843

D017096

Prion Diseases

T051045

T051043

T370039

T842326

T842325

T370038

T370036

T051042

T370041

T051044

T842327

T370037

T370040

NLM (1993)

NLM (2000)

GHR (2014)

T047

http://purl.bioontology.org/ontology/MESH/D019636

http://purl.bioontology.org/ontology/MESH/D002494