Preferred Name |
Myelinolysis, Central Pontine |
Synonyms |
Extrapontine Myelinolysis |
Definitions |
A demyelinating condition affecting the PONS and characterized clinically by an acute progressive QUADRIPLEGIA; DYSARTHRIA; DYSPHAGIA; and alterations of consciousness. Pathologic features include prominent demyelination in the central PONS with sparing of axons and neurons. This condition is usually associated with systemic disorders such as HYPONATREMIA; chronic ALCOHOLISM; LIVER FAILURE; severe BURNS; malignant NEOPLASMS; hemorrhagic PANCREATITIS; HEMODIALYSIS; and SEPSIS. The rapid medical correction of hyponatremia has been cited as a cause of this condition. (From Adams et al., Principles of Neurology, 6th ed, pp1125-6) |
ID |
http://purl.bioontology.org/ontology/MESH/D017590 |
altLabel |
Extrapontine Myelinolysis Myelinolyses, Extrapontine Myelinoclasis, Central Pontine Central Pontine Myelinoclasis Myelinolysis, Extrapontine Extrapontine Myelinoclasis Extrapontine Myelinolyses Myelinoclases, Extrapontine Central Pontine Myelinolysis Extrapontine Myelinoclases Myelinoclasis, Extrapontine Pontine Myelinolysis, Central |
AQL |
BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI |
cui |
C0206083 C0393667 |
DC |
1 |
definition |
A demyelinating condition affecting the PONS and characterized clinically by an acute progressive QUADRIPLEGIA; DYSARTHRIA; DYSPHAGIA; and alterations of consciousness. Pathologic features include prominent demyelination in the central PONS with sparing of axons and neurons. This condition is usually associated with systemic disorders such as HYPONATREMIA; chronic ALCOHOLISM; LIVER FAILURE; severe BURNS; malignant NEOPLASMS; hemorrhagic PANCREATITIS; HEMODIALYSIS; and SEPSIS. The rapid medical correction of hyponatremia has been cited as a cause of this condition. (From Adams et al., Principles of Neurology, 6th ed, pp1125-6) |
DX |
19940101 |
HN |
1994 |
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000401 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000523 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000209 |
Inverse of SIB |
http://purl.bioontology.org/ontology/MESH/D012202 http://purl.bioontology.org/ontology/MESH/D052879 http://purl.bioontology.org/ontology/MESH/D011129 http://purl.bioontology.org/ontology/MESH/D020279 http://purl.bioontology.org/ontology/MESH/D007647 http://purl.bioontology.org/ontology/MESH/D014899 http://purl.bioontology.org/ontology/MESH/D020278 http://purl.bioontology.org/ontology/MESH/D020739 http://purl.bioontology.org/ontology/MESH/D006501 http://purl.bioontology.org/ontology/MESH/D054319 http://purl.bioontology.org/ontology/MESH/D060486 |
Machine permutation |
1994 |
MDA |
19921228 |
MMR |
20090706 |
MN |
C18.452.132.560 C10.314.500 C10.228.140.163.560 |
notation |
D017590 |
prefLabel |
Myelinolysis, Central Pontine |
TERMUI |
T052748 T369623 T052746 T052745 T369624 T052747 |
TH |
NLM (2000) NLM (1994) ORD (2010) |
tui |
T047 |
subClassOf |