Preferred Name |
Neuroectodermal Tumors, Primitive, Peripheral |
Synonyms |
Neuroectodermal Neoplasm, Peripheral Primitive |
Definitions |
A group of highly cellular primitive round cell neoplasms which occur extracranially in soft tissue and bone and are derived from embryonal neural crest cells. These tumors occur primarily in children and adolescents and share a number of characteristics with EWING SARCOMA. |
ID |
http://purl.bioontology.org/ontology/MESH/D018241 |
altLabel |
Neuroectodermal Neoplasm, Peripheral Primitive Extracranial Primitive Neuroectodermal Tumor Peripheral Neuroectodermal Tumor Neuroepithelioma, Peripheral Peripheral Neuroepitheliomas Peripheral Neuroepithelioma Neuroectodermal Tumor, Peripheral Neuroectodermal Tumors, Peripheral Peripheral Primitive Neuroectodermal Tumors (pPNET) Peripheral Primitive Neuroectodermal Tumors Primitive Neuroectodermal Tumor, Extracranial Peripheral Neuroectodermal Tumors Tumor, Peripheral Neuroectodermal Peripheral Primitive Neuroectodermal Neoplasm Neuroectodermal Tumor, Peripheral Primitive Neuroepitheliomas, Peripheral Tumors, Peripheral Neuroectodermal |
AN |
coordinate IM with precoordinated organ/neoplasm term (IM) |
AQL |
BL BS CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SC SU TH UL UR VE VI |
cui |
C0684337 |
DC |
1 |
definition |
A group of highly cellular primitive round cell neoplasms which occur extracranially in soft tissue and bone and are derived from embryonal neural crest cells. These tumors occur primarily in children and adolescents and share a number of characteristics with EWING SARCOMA. |
DX |
19940101 |
HN |
2000(1994) |
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000401 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000737 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000556 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000648 http://purl.bioontology.org/ontology/MESH/Q000523 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000098 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000209 |
Inverse of RO | |
Inverse of SIB | |
Machine permutation |
2000(1994); see NEUROECTODERMAL TUMOR, PERIPHERAL 1994-1999; NEUROEPITHELIOMA was heading 1966-1999 |
MDA |
19930625 |
MMR |
20160208 |
MN |
C04.557.465.625.600.590.650 C04.557.470.670.590.650 C04.557.580.625.600.590.650 |
notation |
D018241 |
prefLabel |
Neuroectodermal Tumors, Primitive, Peripheral |
TERMUI |
T372801 T812400 T372807 T372805 T054520 T372803 T372804 T372808 T365792 T372802 |
TH |
NLM (2000) NLM (1994) OMIM (2013) |
tui |
T191 |
subClassOf |
Delete | Mapping To | Ontology | Source |
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There are currently no mappings for this class. |