Preferred Name |
Lymphoma, Mantle-Cell |
Synonyms |
Centrocytic Small-Cell Lymphomas |
Definitions |
A form of non-Hodgkin lymphoma having a usually diffuse pattern with both small and medium lymphocytes and small cleaved cells. It accounts for about 5% of adult non-Hodgkin lymphomas in the United States and Europe. The majority of mantle-cell lymphomas are associated with a t(11;14) translocation resulting in overexpression of the CYCLIN D1 gene (GENES, BCL-1). |
ID |
http://purl.bioontology.org/ontology/MESH/D020522 |
altLabel |
Centrocytic Small-Cell Lymphomas Mantle-Zone Lymphoma Mantle Cell Lymphoma Small-Cell Lymphomas, Centrocytic Lymphoma, Lymphocytic, Intermediate Lymphoma, Lymphocytic, Diffuse, Poorly-Differentiated Diffuse Lymphocytic Lymphoma, Poorly Differentiated Mantle-Cell Lymphomas Mantle Zone Lymphoma Lymphocytic Lymphoma, Diffuse, Poorly-Differentiated Lymphoma, Small-Cell, Centrocytic Lymphoma, Mantle-Zone Centrocytic Small-Cell Lymphoma Lymphomas, Mantle-Cell Lymphoma, Mantle Cell Diffuse Lymphocytic Lymphoma, Poorly-Differentiated Mantle-Zone Lymphomas Lymphoma, Centrocytic Small-Cell Lymphomas, Centrocytic Small-Cell Lymphomas, Mantle-Zone Lymphocytic Lymphoma, Diffuse, Poorly Differentiated Lymphoma, Centrocytic Small Cell Small-Cell Lymphoma, Centrocytic Lymphoma, Lymphocytic, Diffuse, Intermediate Differentiated Mantle-Cell Lymphoma |
AQL |
BL CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UL UR VE VI |
cui |
C0751958 C0334634 |
DC |
1 |
definition |
A form of non-Hodgkin lymphoma having a usually diffuse pattern with both small and medium lymphocytes and small cleaved cells. It accounts for about 5% of adult non-Hodgkin lymphomas in the United States and Europe. The majority of mantle-cell lymphomas are associated with a t(11;14) translocation resulting in overexpression of the CYCLIN D1 gene (GENES, BCL-1). |
DX |
20000101 |
FX |
D019938 D019940 |
HN |
2000; for LYMPHOMA, LYMPHOCYTIC, DIFFUSE, INTERMEDIATE; LYMPHOCYTIC LYMPHOMA, DIFFUSE, POORLY-DIFFERENTIATED; LYMPHOMA, CENTROCYTIC SMALL-CELL; LYMPHOMA, LYMPHOCYTIC, DIFFUSE, POORLY-DIFFERENTIATED; & LYMPHOMA, SMALL-CELL, CENTROCYTIC use LYMPHOMA, SMALL CLEAVED-CELL, DIFFUSE 1991-1999 |
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000401 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000737 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000648 http://purl.bioontology.org/ontology/MESH/Q000523 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000209 |
Inverse of RO | |
Inverse of SIB |
http://purl.bioontology.org/ontology/MESH/D016399 http://purl.bioontology.org/ontology/MESH/D008224 |
Machine permutation |
2000; for LYMPHOMA, LYMPHOCYTIC, DIFFUSE, INTERMEDIATE; LYMPHOCYTIC LYMPHOMA, DIFFUSE, POORLY-DIFFERENTIATED; LYMPHOMA, CENTROCYTIC SMALL-CELL; LYMPHOMA, LYMPHOCYTIC, DIFFUSE, POORLY-DIFFERENTIATED; & LYMPHOMA, SMALL-CELL, CENTROCYTIC see LYMPHOMA, SMALL CLEAVED-CELL, DIFFUSE 1991-1999 |
MDA |
19991108 |
MMR |
20180629 |
MN |
C15.604.515.569.480.525 C20.683.515.761.480.525 C04.557.386.480.525 |
notation |
D020522 |
prefLabel |
Lymphoma, Mantle-Cell |
TERMUI |
T049076 T362653 T372756 T049075 T049074 T049079 T049073 T358571 T362502 T362503 T049078 |
TH |
NLM (1991) NLM (2000) |
tui |
T191 T047 |
subClassOf |