| Preferred Name |
Mastocytosis, Cutaneous |
| Synonyms |
Mastocytoses, Bullous |
| Definitions |
A form of cutaneous mastocytosis that is characterized by the large fluid-filled lesions. |
| ID |
http://purl.bioontology.org/ontology/MESH/D034701 |
| altLabel |
Mastocytoses, Bullous Bullous Mastocytosis Mastocytoses, Cutaneous Skin Mastocytoses Mastocytosis, Diffuse Cutaneous Mastocytosis, Skin Skin Mastocytosis Cutaneous Mastocytosis, Diffuse Cutaneous Mastocytoses, Diffuse Mastocytoses, Skin Bullous Mastocytoses Cutaneous Mastocytoses Mastocytosis, Bullous Cutaneous Mastocytosis |
| AN |
MACULOPAPULAR CUTANEOUS MASTOCYTOSIS see URTICARIA PIGMENTOSA is also available |
| AQL |
BL BS CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SC SU TH UL UR VE VI |
| cui |
C0024901 C0024900 C1136033 |
| DC |
1 |
| definition |
A form of cutaneous mastocytosis that is characterized by the large fluid-filled lesions. A form of cutaneous mastocytosis that is characterized by a diffuse erythrodermic rash rather than the maculopapular infiltrates seen in URTICARIA PIGMENTOSA. Skin lesions due to abnormal infiltration of MAST CELLS. Cutaneous mastocytosis is confined to the skin without the involvement of other tissues or organs, and is mostly found in children. The three major variants are: URTICARIA PIGMENTOSA; diffuse cutaneous mastocytosis; and SOLITARY MASTOCYTOMA OF SKIN. |
| DX |
20030101 |
| HN |
2003; for MASTOCYTOSIS, BULLOUS use URTICARIA PIGMENTOSA 1987-2002; for MASTOCYTOSIS, DIFFUSE CUTANEOUS use URTICARIA PIGMENTOSA 1987-2002 |
| Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000401 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000737 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000556 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000648 http://purl.bioontology.org/ontology/MESH/Q000523 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000098 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000209 |
| Inverse of SIB |
http://purl.bioontology.org/ontology/MESH/D034721 |
| Machine permutation |
2003; for MASTOCYTOSIS, BULLOUS see URTICARIA PIGMENTOSA 1987-2002; for MASTOCYTOSIS, DIFFUSE CUTANEOUS see URTICARIA PIGMENTOSA 1987-2002 |
| Mapped from | |
| MDA |
20020702 |
| MMR |
20170620 |
| MN |
C17.800.508.473 C04.557.450.565.465.500 |
| notation |
D034701 |
| prefLabel |
Mastocytosis, Cutaneous |
| TERMUI |
T042660 T042661 T476062 T471633 T474465 |
| TH |
UNK (19XX) NLM (2003) |
| tui |
T191 T047 |
| subClassOf |