Medical Subject Headings

Last uploaded: November 5, 2019
Preferred Name

gamma-Butyrobetaine Dioxygenase

Synonyms

Trimethylaminobutyrate Hydroxylase

Definitions

An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN.

ID

http://purl.bioontology.org/ontology/MESH/D050563

altLabel

Trimethylaminobutyrate Hydroxylase

Hydroxylase, Butyrobetaine

Dioxygenase, gamma-Butyrobetaine

gamma-Butyrobetaine,2-Oxoglutarate Dioxygenase

gamma-Butyrobetaine, 2-Oxoglutarate Dioxygenase

gamma Butyrobetaine,2 Oxoglutarate Dioxygenase

Hydroxylase, Trimethylaminobutyrate

Dioxygenase gamma-Butyrobetaine, 2-Oxoglutarate

gamma Butyrobetaine, 2 Oxoglutarate Dioxygenase

Dioxygenase, gamma-Butyrobetaine,2-Oxoglutarate

4-Trimethylaminobutyrate, 2-Oxoglutarate Oxygen Oxidoreductase (3-Hydroxylating)

gamma-Butyrobetaine Hydroxylase

Hydroxylase, gamma-Butyrobetaine

2-Oxoglutarate Dioxygenase gamma-Butyrobetaine

gamma Butyrobetaine Hydroxylase

gamma Butyrobetaine Dioxygenase

Butyrobetaine Hydroxylase

AQL

AD AE AI AN BI BL CF CH CL CS DE DF EC GE HI IM IP ME PD PH PK PO RE SD ST TO TU UL UR

cui

C0061031

DC

1

definition

An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN.

DX

20060101

HN

2006(1980); use KETOGLUTARIC ACID 1973-1974, BETAINE 1972-1979, BUTYRATES 1974-1979, & AMINOBUTYRIC ACID 1970-1974

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000032

http://purl.bioontology.org/ontology/MESH/Q000138

http://purl.bioontology.org/ontology/MESH/Q000737

http://purl.bioontology.org/ontology/MESH/Q000493

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000506

http://purl.bioontology.org/ontology/MESH/Q000187

http://purl.bioontology.org/ontology/MESH/Q000096

http://purl.bioontology.org/ontology/MESH/Q000037

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000592

http://purl.bioontology.org/ontology/MESH/Q000528

http://purl.bioontology.org/ontology/MESH/Q000008

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000648

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000633

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000009

http://purl.bioontology.org/ontology/MESH/Q000302

http://purl.bioontology.org/ontology/MESH/Q000502

http://purl.bioontology.org/ontology/MESH/Q000494

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000600

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000172

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000627

Inverse of RB

EC 1.14.11.1

Inverse of SIB

http://purl.bioontology.org/ontology/MESH/D003577

http://purl.bioontology.org/ontology/MESH/D050601

http://purl.bioontology.org/ontology/MESH/D004156

http://purl.bioontology.org/ontology/MESH/D006419

http://purl.bioontology.org/ontology/MESH/D050565

http://purl.bioontology.org/ontology/MESH/D050603

http://purl.bioontology.org/ontology/MESH/D044943

http://purl.bioontology.org/ontology/MESH/D015109

http://purl.bioontology.org/ontology/MESH/D014446

http://purl.bioontology.org/ontology/MESH/D011451

http://purl.bioontology.org/ontology/MESH/D050564

http://purl.bioontology.org/ontology/MESH/D014365

http://purl.bioontology.org/ontology/MESH/D064417

http://purl.bioontology.org/ontology/MESH/D064828

http://purl.bioontology.org/ontology/MESH/D008240

http://purl.bioontology.org/ontology/MESH/D010651

http://purl.bioontology.org/ontology/MESH/D004299

Machine permutation

2006; GAMMA-BUTYROBETAINE DIOXYGENASE was indexed under MIXED FUNCTION OXYGENASES 1980-2005, KETOGLUTARIC ACID 1973-1974, BETAINE 1972-1980, BUTYRATES 1974-1979, & AMINOBUTYRIC ACID 1970-1974

Mapped from

http://purl.bioontology.org/ontology/MESH/C513904

MDA

20050630

MN

D08.811.682.690.708.401

notation

D050563

prefLabel

gamma-Butyrobetaine Dioxygenase

TERMUI

T630677

T102680

T102676

T102678

T102677

T629666

T102679

TH

NLM (2006)

tui

T116

T126

subClassOf

http://purl.bioontology.org/ontology/MESH/D006899

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http://purl.obolibrary.org/obo/PR_000004662 Protein Ontology LOOM