National Cancer Institute Thesaurus

Last uploaded: February 21, 2019
Preferred Name

Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor

ID

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C27291

ALT_DEFINITION

A group of cancers that includes Ewing tumor of bone (ETB or Ewing sarcoma of bone), extraosseous Ewing (EOE) tumors, primitive neuroectodermal tumors (PNET or peripheral neuroepithelioma), and Askin tumors (PNET of the chest wall). These tumors all come from the same type of stem cell.

code

C27291

Concept_In_Subset

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C116977

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C103038

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C102905

Contributing_Source

CTEP

CTRP

DEFINITION

A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms.

Display_Name

Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor

FULL_SYN

Ewing sarcoma family of tumors

Ewing sarcoma/Peripheral PNET

Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor

Ewing Family of Tumors

Ewing's Family of Tumours

EFTs

Tumors of the Ewing's Family

Ewing's Family of Tumors

Tumors of Ewing's Family

label

Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor

Legacy_Concept_Name

Ewing_s_Sarcoma_Peripheral_Primitive_Neuroectodermal_Tumor

Neoplastic_Status

Malignant

Preferred_Name

Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor

prefixIRI

C27291

prefLabel

Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor

Semantic_Type

Neoplastic Process

UMLS_CUI

C0684337

subClassOf

http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C3264

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