Medical Subject Headings

Last uploaded: November 5, 2019
Preferred Name

Pheochromocytoma

Synonyms

Extra-Adrenal Pheochromocytomas

Definitions

A usually benign, well-encapsulated, lobular, vascular tumor of chromaffin tissue of the ADRENAL MEDULLA or sympathetic paraganglia. The cardinal symptom, reflecting the increased secretion of EPINEPHRINE and NOREPINEPHRINE, is HYPERTENSION, which may be persistent or intermittent. During severe attacks, there may be HEADACHE; SWEATING, palpitation, apprehension, TREMOR; PALLOR or FLUSHING of the face, NAUSEA and VOMITING, pain in the CHEST and ABDOMEN, and paresthesias of the extremities. The incidence of malignancy is as low as 5% but the pathologic distinction between benign and malignant pheochromocytomas is not clear. (Dorland, 27th ed; DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1298)

ID

http://purl.bioontology.org/ontology/MESH/D010673

altLabel

Extra-Adrenal Pheochromocytomas

Pheochromocytoma, Extra-Adrenal

Extra-Adrenal Pheochromocytoma

Pheochromocytoma, Extra Adrenal

Pheochromocytomas

Pheochromocytomas, Extra-Adrenal

AN

benign or malignant; coord IM with usually ADRENAL GLAND NEOPLASMS (IM)

AQL

BL BS CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SC SU TH UL UR VE VI

cui

C1257877

C0031511

DC

1

definition

A usually benign, well-encapsulated, lobular, vascular tumor of chromaffin tissue of the ADRENAL MEDULLA or sympathetic paraganglia. The cardinal symptom, reflecting the increased secretion of EPINEPHRINE and NOREPINEPHRINE, is HYPERTENSION, which may be persistent or intermittent. During severe attacks, there may be HEADACHE; SWEATING, palpitation, apprehension, TREMOR; PALLOR or FLUSHING of the face, NAUSEA and VOMITING, pain in the CHEST and ABDOMEN, and paresthesias of the extremities. The incidence of malignancy is as low as 5% but the pathologic distinction between benign and malignant pheochromocytomas is not clear. (Dorland, 27th ed; DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1298)

DX

19660101

FX

D018814

D018813

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000401

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000737

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000556

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000648

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000098

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000469

Inverse of RO

http://purl.bioontology.org/ontology/MESH/D018814

http://purl.bioontology.org/ontology/MESH/D018813

Inverse of SIB

http://purl.bioontology.org/ontology/MESH/D010236

Mapped from

http://purl.bioontology.org/ontology/MESH/C566807

http://purl.bioontology.org/ontology/MESH/C563522

MDA

19990101

MMR

20120703

MN

C04.557.465.625.650.700.725

C04.557.580.625.650.700.725

notation

D010673

prefLabel

Pheochromocytoma

TERMUI

T530045

T031545

TH

NLM (2004)

NLM (1966)

ORD (2010)

OMIM (2013)

tui

T191

subClassOf

http://purl.bioontology.org/ontology/MESH/D010235

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/OMIM/MTHU004455 Online Mendelian Inheritance in Man CUI
http://purl.bioontology.org/ontology/OMIM/185470 Online Mendelian Inheritance in Man CUI
http://purl.bioontology.org/ontology/OMIM/171300 Online Mendelian Inheritance in Man CUI
http://purl.bioontology.org/ontology/OMIM/171300 Online Mendelian Inheritance in Man LOOM
http://purl.obolibrary.org/obo/DOID_0050771 Human Disease Ontology 123 LOOM
http://purl.bioontology.org/ontology/OMIM/608537 Online Mendelian Inheritance in Man CUI
http://purl.bioontology.org/ontology/OMIM/605995 Online Mendelian Inheritance in Man CUI
http://purl.bioontology.org/ontology/OMIM/164761 Online Mendelian Inheritance in Man CUI
http://purl.bioontology.org/ontology/OMIM/MTHU004454 Online Mendelian Inheritance in Man CUI
http://purl.bioontology.org/ontology/OMIM/602690 Online Mendelian Inheritance in Man CUI
http://purl.bioontology.org/ontology/OMIM/MTHU015027 Online Mendelian Inheritance in Man CUI
http://purl.bioontology.org/ontology/OMIM/MTHU015027 Online Mendelian Inheritance in Man LOOM
http://purl.bioontology.org/ontology/MEDLINEPLUS/C0031511 MedlinePlus Health Topics CUI
http://purl.bioontology.org/ontology/MEDLINEPLUS/C0031511 MedlinePlus Health Topics LOOM
http://purl.obolibrary.org/obo/MPATH_377 Human Phenotype Ontology China LOOM